BCH 206
Amino Acids Metabolism
1 Unit(s) (LH 15)
Course Description
At the end of this course, students should be able to:
1. define the metabolism of amino acid;
2. outline transamination, oxidative deamination, decarboxylation;
3. discuss the urea cycle and its biochemical importance;
4. explain inborn errors of metabolism of some amino acids;
5. outline phenylketonuria, tyrosinosis, alkaptonuria, albinism, cystinuria; and
6. apply biochemical knowledge in the clinics.
Course Outline
Introduction to the metabolism of amino acid. Transamination, oxidative deamination,
decarboxylation. The urea cycle and its biochemical importance’s. Inborn errors of metabolism
of some amino acids, phenylketonuria, tyrosinosis, alkaptonuria, albinism, cystinuria.